{'fraction_non_alphanumeric': 0.024193548387096774, 'fraction_numerical': 0.0, 'mean_word_length': 5.744565217391305, 'pattern_counts': {'":': 0, '<': 0, '<?xml version=': 0, '>': 0, 'https://': 0, 'lorem ipsum': 0, 'www.': 0, 'xml': 0}, 'pii_count': 0, 'substrings_counts': 0, 'word_list_counts': {'cursed_substrings.json': 0, 'profanity_word_list.json': 0, 'sexual_word_list.json': 0, 'zh_pornsignals.json': 0}}
[Semantic dementia: clinical profile and cognitive-neuropsychological relevance].

Semantic Dementia (SD) represents a rare variant of presenile primary degenerative diseases of "frontotemporal lobar degenerations" (FTLD). SD is characterized by anterior-temporal atrophy and a selective semantic deficit. Neuropsychological impairment either bears on fluent aphasia with marked naming and comprehension difficulties or on a disorder of object recognition or on both. Behavioural alterations such as stereotyped behaviour and change in food preference become prominent as the disease progresses and are interpreted as a correlative for the pathological spreading to frontal structures. Since SD is often misclassified as Alzheimer's disease (AD), but calls for a different management, diagnostic consensus criteria by Neary and colleagues are depicted. The neuropsychological profile is described in detail and complemented by a case report. Implications from the dissociation of disturbed memory systems of SD (semantic) and AD (episodic) for models of long-term memory are discussed in terms of connectivity in the medial temporal lobe. SD can contribute to a better understanding of the structure and organisation of the semantic system.