The Ehlers-Danlos Syndrome (EDS) is a rare connective tissue disorder characterised by fragility of the soft connective tissues and widespread manifestations in skin, ligaments, joints, blood vessels and internal organs. We report a case of a 12-year-old boy, previously diagnosed with kyphoscoliosis-type EDS (type VI), presenting with a left brachial artery pseudo-aneursym with history of multiple spontaneous and post-traumatic arterial ruptures. Surgical management of this patient was performed successfully by primary repair of brachial artery lesion.
The Ehlers - Danlos Syndrome ( EDS ) is a rare connective tissue disorder characterised by fragility of the soft connective tissues and widespread manifestations in skin , ligaments , joints , blood vessels and internal organs . We report a case of a 12-year - old boy , previously diagnosed with kyphoscoliosis - type EDS ( type VI ) , presenting with a left brachial artery pseudo - aneursym with history of multiple spontaneous and post - traumatic arterial ruptures . Surgical management of this patient was performed successfully by primary repair of brachial artery lesion .
What tissue is most affected in Ehlers-Danlos syndromes?
What tissue is most affected in Ehlers - Danlos syndromes ?
connective tissue
connective tissue