pediatrics
Hyper IgD Syndrome
Treatment of Hyper IgD Syndrome
For preventing attacks,anakinraorcanakinumab For symptoms, nonsteroidal anti-inflammatory drugs (NSAIDs), corticosteroids, andanakinra every 4 weeks are proved to prevent attacks ( Treatment references ). Patients can expect to have recurrent bouts of fever throughout their life, although episodes tend to become less frequent after adolescence. has been used successfully ( Treatment references ). 1.De Benedetti F, Gattorno M, Anton J, et al:Canakinumabfor the treatment of autoinflammatory recurrent fever syndromes.N Engl J Med378(20):1908–1919, 2018. doi: 10.1056/NEJMoa1706314 2.Ashari KA, Hausmann JS, Dedeoglu F: Update on autoinflammatory diseases.Curr Opin Rheumatol35(5):285-292, 2023. doi: 10.1097/BOR.0000000000000953 