pulmonary disorders
Idiopathic Pleuroparenchymal Fibroelastosis
Symptoms and Signs of Idiopathic PPFE
The median age of presentation is around 57 years, with no sex predilection. Most patients with idiopathic pleuroparenchymal fibroelastosis do not smoke. Patients often report a history of recurrent infections, shortness of breath, and dry cough. Pneumothorax is common during the course of the disease. 