lung and airway disorders
Idiopathic Pulmonary Fibrosis
Introduction
Idiopathic pulmonary fibrosis is the most common form of idiopathic interstitial pneumonia. Idiopathic pulmonary fibrosis affects mostly people over the age of 50 years, usually people who have formerly smoked. People may cough, have difficulty breathing, and feel tired. Pulmonary rehabilitation, lung transplantation, and drugs such aspirfenidoneandnintedanib, are treatments. (See also Overview of Idiopathic Interstitial Pneumonias and In idiopathic pulmonary fibrosis, the lungs develop progressive scarring for unknown reasons. There seems to be a genetic component because some families have more than one person affected by the disorder. Specific gene mutations have been identified in some people with idiopathic pulmonary fibrosis. 