genitourinary disorders
Pseudohypoaldosteronism Type I
Introduction
Pseudohypoaldosteronism type I is a group of rare hereditary disorders that cause the kidneys to retain too much potassium but excrete too much sodium and water, leading to hypotension. Symptoms may result from hypotension, hypovolemia, hyponatremia, and hyperkalemia. Treatment is with a high-sodium diet and sometimesfludrocortisone. There are 3 types of pseudohypoaldosteronism: Autosomal recessive pseudohypoaldosteronism type I Autosomal dominant pseudohypoaldosteronism type I Pseudohypoaldosteronism type II Inheritance is autosomal recessive or autosomal dominant. Pseudohypoaldosteronism type I resembles other forms of hypoaldosteronism except thataldosteronelevels are high. The very rare pseudohypoaldosteronism type II is not discussed here. 