cardiovascular disorders
Non Compaction Cardiomyopathy
Key Points
Non-compaction cardiomyopathies are genetic cardiac disorders that cause heart failure, arrhythmias, heart blocks, and thromboembolic disease. Diagnosis is based on clinical factors, arrhythmias, cardiac imaging, and genetic testing. First-degree family members have a significant risk of disease and require screening. Treatment may require an implantable cardioverter-defibrillator (ICD), antiarrhythmic drugs, anticoagulation, and/or heart failure drugs. 