genitourinary disorders
Congenital Renal Cystic Dysplasia
Introduction
Congenital renal cystic dysplasia is a broad category of congenital malformations involving metanephric malformation or congenital obstructive uropathies. (See also Overview of Cystic Kidney Disease .) ). Associated urologic abnormalities may include ureteropelvic and ureterovesicular junction obstruction, Neurogenic Bladder ureterocele, posterior urethral valves, and Symptoms and signs vary by how much renal parenchyma is preserved and whether involvement is unilateral or bilateral. Some degree of renal insufficiency or Chronic Kidney Disease may develop. Congenital renal cystic dysplasia is commonly discovered by ultrasonography prenatally or during early childhood. Prognosis is highly unpredictable due to an inability to quantify residual functional parenchyma. Treatment is surgical correction of any associated genitourinary abnormalities and, if renal insufficiency or renal failure is present, Overview of Renal Replacement Therapy . 