genitourinary disorders
Congenital Nephrotic Syndromes
Other congenital nephrotic syndromes
Several other rare congenital nephrotic syndromes are now genetically characterized. These disorders include Corticosteroid-resistant nephrotic syndrome (defectiveNPHS2gene coding for podocin) Familial Focal Segmental Glomerulosclerosis (defective Denys-Drash syndrome, which is characterized by diffuse mesangial sclerosis, male pseudohermaphroditism, and Wilms Tumor (defective 