pediatrics
Double Outlet Right Ventricle
Key Points
In double outlet right ventricle (DORV), both the aorta and pulmonary valve connect to the right ventricle. DORV has a wide spectrum of anatomy and physiology depending on the size and location of the ventricular septal defect (VSD) and the presence and degree of Pulmonic Stenosis . Diagnosis is with chest x-ray, MRI, CT, ECG, echocardiography, and cardiac catheterization. During the newborn period, prostaglandins might be needed for severe cyanosis; heart failure treatment may also be needed. Surgery is inevitably required; in the most common type, complete repair is possible. 