pediatrics
Congenitally Corrected Transposition of the Great Arteries
Introduction
In congenitally corrected transposition of the great arteries (CCTGA), the right atrium enters a right-sided morphologic left ventricle, which gives rise to the pulmonary artery, and the left atrium connects to a left-sided morphologic right ventricle, which then leads to the aorta. This flow pattern results in a physiologic correction of the circulation despite the abnormal chamber connections. There is a wide range of clinical manifestations due to the multiple associated anomalies. Diagnosis is by physical examination, ECG, imaging, and cardiac catheterization. Treatment is medical, surgical, and with rhythm devices. (See also Overview of Congenital Cardiovascular Anomalies .) Congenitally corrected transposition (levo-transposition) of the great arteries is relatively rare and accounts for about 0.5% of congenital cardiac anomalies. Associated anomalies are present in the majority of patients, including Ventricular Septal Defect (VSD) (VSD), 