nutritional disorders
Carnitine Deficiency
Treatment of Carnitine Deficiency
Avoidance of fasting and strenuous exercise Dietary interventions, based on cause Carnitine deficiency due to inadequate dietary intake, increased requirements, excess losses, decreased synthesis, or (sometimes) enzyme deficiencies can be treated by giving L-carnitine 25 mg/kg orally every 6 hours. All patients must avoid fasting and strenuous exercise. Consuming uncooked cornstarch at bedtime prevents early morning hypoglycemia. Some patients require supplementation with medium-chain triglycerides and essential fatty acids (eg, linoleic acid, linolenic acid). Patients with a Beta-Oxidation Cycle Disorders require a high-carbohydrate, low-fat diet. 