A child presents with hepatomegaly and hypoglycemia. There is no improvement in blood sugar even after administration of epinephrine. What is the likely diagnosis –
Von girke's disease
Anderson's disease
Pompe's disease
Mc Ardle's disease
Amongst the given options only Von Gierke's disease presents with hepatomegaly and hypoglycemia.

"A diagnosis of type I glycogen storage disease (Von Gierke's disease) should be suspected whenever there is hepatomegaly with hypoglycemia that is unresponsive to glucagon or epinephrine".