Highest mortality in pregnancy
Fallot's tetrologv
Coarctation of aorta
Marfan’s syndrome
Eisenmenger syndrome
Eisenmenger syndrome

These patients have pulmonary hypertension with shunt (right to left) through an open ductus or ASD or VSD.
Maternal mortality is high i.e. 50% & so is a perinatal loss (50%).
Fallot’s tetralogy, coarctaion of aorta & Marfan's syndrome hav mortality’ rate of 5-10%, 3-9% & 25% respectively