Features of Peutz-Jeghers syndrome are all except
Autosomal dominant
Mucocutaneous pigmentation
Hamaomatous polyp
High risk of malignacy
Peutz Jeghers syndrome is an autosomal dominant defect, characterised by hamaomatous intestinal polyposis and melanotic pigmentation of lips , mouth and genitalia. It DONOT UNDERGO MALIGNANT TRANSFORMATION unless a coexistant adenoma present. Reference : Harsh Mohan textbook of pathology, 7th edition.Pg no.566
Haematology