A baby with flat face, low set ears, micrognathia has limb deformities . and bilateral renal agenesis . There is antenatal history of oligohydromnios . The baby died of pulmonary hypoplasia what is the most probable diagnosis?
Polycystic Kidney disease
Prune belly syndrome
Potter syndrome
Multicystic dysplastic kidney
Potter syndrome :
potter facies : Flat face, flat nose, low set ears, receding chin. Bilateral renal agenesis. Most common cause of death in pulmonary hypoplasia.