Hepatomegaly is a feature of all of the following, EXCEPT:
Hurler's Disease
Hepatic porphyrias
Von Gierke's Disease
Nieman Pick Disease
Frank Hepatomegaly is rare in hepatic porphyrias. Although hepatomegaly may occasionally be seen in hepatic porphyrias, frank hepatomegaly is rare and not a prominent manifestation of hepatic porphyria. Hepatic porphyria is therefore the single best answer by exclusion. Hepatomegaly is a prominent manifestation of Hurler's syndrome, Nieman Pick disease and Von Girke's Disease. Ref: Harrison's Internal Medicine, 16th Edition, Pages 2316, 2320; Oxford Textbook of Medicine, 4th Edition, Page 69; Gastrointestinal and Liver Disease By Feldman, 8th Edition, Page 1623; Harrison's Principles of Internal Medicine, 18th Edition, Chapters 361-362